摘要
目的：加深对窒息性胸廓发育不良（ATD）影像表现的认识。方法：通过4例ATD X线和CT影像分析，结合临床资料及有关文献加以讨论。结果： ①ATD是一种少见的常染色体隐性遗传性骨软骨发育不良疾病。②X线主要表现：胸廓狭长，肋骨短，肋骨头膨大；髂翼呈方形，股骨头骨骺提前骨化；长骨短，干骺端增宽；掌指骨短粗，锥形骨骺及赘生指。结论：对反复肺部感染的患儿，应进行影像学检查，早日明确诊断，为临床治疗提供依据。
Abstract
Objective: To promote the understanding of the image features of asphyxiating thoracic dysplasia(ATD). Methods: X-ray films and CT image features of four ATD were studied combining with clinical and relative literatures. Result: ATD is an uncommon autosomal recessive hereditary disorder of osteochondrodysplasia. The main findings of ATD are as follows: a narrow thorax, short ribs, the anterior ends of the ribs are widened and cupped; the pelvis also shows flaring ala of the ilium and early ossification of the centers for the capital femoral epiphyses; extremity deformities include shortening of the long tubular bone, metaphyseal irregularities and windening, the shortening of tubular bones of the hands with cone-shaped epiphyses and polydactylism. Conclusion: The children who suffer from pneumonia repeatedly should perform X-ray examination to help make correct diagnosis on time.
关键词
胸部疾病 /
放射摄影术 /
胸部 /
体层摄影术 /
X线计算机
Key words
thoracic diseases /
radiography /
thoracic /
tomography /
X-ray computed
刘 凯;衣 蕾;王丽华;鲍爱华.
窒息性胸廓发育不良的影像表现（附4例报告）[J]. 中国临床医学影像杂志. 2006, 17(11): 613-615
LIU Kai;YI Lei;WANG Li-hua;BAO Ai-hua.
The imaging features of asphyxiating thoracic dysplasia(report of four cases)[J]. Journal of China Clinic Medical Imaging. 2006, 17(11): 613-615
中图分类号：
Ｒ655.1
Ｒ814.41
Ｒ814.42
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