目的：探讨成人先天性肺囊性腺瘤样畸形（Congenital cystic adenomatoid malformation，CCAM）的CT表现。方法：收集2005年3月—2015年11月共9例于我院就诊患者。术前行CT扫描或CT增强扫描，术后病理证实为CCAM，分析CT表现与术后病理结果。结果：本实验9例患者，7例病变位于右肺，2例位于左肺；其中7例累及单个肺叶，仅2例累及两个肺叶。CT表现9例病变中8例为大囊型（直径>2 cm），仅1例为小囊型（直径<2 cm）。8例大囊型中6例为单囊或少囊型（≤3个），壁光滑，无突起，多见腔内积液；2例为多囊结构（>3个），囊壁不光滑，可见脊样突起，多发分隔。1例小囊型病变呈蜂窝状改变，囊大小较均匀，均小于2 cm。9例患者均接受手术切除，病理结果8例大囊型均为StockerⅠ型，1例小囊型符合StockerⅡ。结论：CCAM的CT表现具有一定的特异性，并且与病理分型相关，对患者术前正确诊断具有一定价值。
Abstract
Objective: To investigate the CT manifestation of congenital cystic adenomatoid malformation(CCAM) of lung in adult. Methods: From March 2005 to November 2015, 9 patients with CCAM confirmed by postoperative pathology underwent CT scanning or enhanced CT scanning preoperatively. The CT manifestation and pathological style were analyzed. Results: The lesions of 7 cases were in the right lung, 2 cases in the left lung; 7 cases involved a single lobe, only 2 cases involved two lobes. The CT manifestations of 9 cases with CCAM included macrocystic type(diameter >2 cm) in 8 cases and microcystic type(diameter <2 cm) in 1 case. 6 cases of the macrocystic type contained less than 3 cysts with smooth wall, filled fluid. 2 cases of the macrocystic type were polycystic structure(>3), and the cyst wall was not smooth, with ridge-like protrusions and multiple separation. 1 case of microcystic type was honeycomb structures with homogenous cyst size(<2 cm). Finally, pathological results of 8 macrocystic cases were Stocker’s typeⅠ, the microcystic case was Stocker’s typeⅡ. Conclusion: The CT manifestations of CCAM had a certain characteristics, and might predict the pathological type. CT examination was useful for the preoperative diagnosis of CCAM.
关键词
囊腺瘤样畸形 /
肺 /
先天性；体层摄影术 /
螺旋计算机
Key words
Cystic adenomatoid malformation of lung, congenital /
tomography, spiral computed
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