目的：探讨三血管气管切面在诊断胎儿右位主动脉弓中的应用价值。方法：回顾性分析61例在我院产前超声检查中被诊断为右位主动脉弓的胎儿，总结并分析其在三血管气管切面的超声声像图特点，随访观察其临床结局。结果：61例产前超声诊断为右位主动脉弓的胎儿，其中单纯性右位主动脉弓41例，双主动脉弓2例，右位主动脉弓伴心内畸形14例，右位主动脉弓伴心外畸形2例，右位主动脉弓同时合并心内和心外畸形2例。39例活产胎儿产后证实产前诊断，5例右位主动脉弓合并其他严重畸形的胎儿选择引产（其中4例尸检后病理结果证实产前诊断，1例引产后未做尸检），2例正在密切随访中，1例产后超声心动图结果与产前超声诊断结果不符，14例失访。结论：产前超声扫查三血管气管切面是诊断胎儿右位主动脉弓的可靠方法，单纯性胎儿右位主动脉弓可能不引起明显的临床症状。
Abstract
Objective: To investigate the value of three-vessel-trachea view in the diagnosis of fetal right aortic arch. Methods: Ultrasonic characteristics in three-vessel-trachea view and clinical outcome of 61 fetuses with right aortic arch diagnosed by prenatal ultrasound in our hospital were retrospectively analyzed. Results: Sixty-one cases of fetal right aortic arch were diagnosed by prenatal ultrasound, with simple right aortic arch in 41 cases, double aortic arch in 2 cases, right aortic arch with cardiac abnormalities in 14 cases, right aortic arch with extracardiac malformations in 2 cases, and right aortic arch combined with cardiac and extracardiac malformations at the same time in 2 cases. Thirty-nine cases of live births postpartum confirmed prenatal diagnosis. Five cases of right aortic arch combined with other serious malformations chose induced labor(including 4 cases of autopsy results confirming the prenatal diagnosis, 1 case of induced labor without autopsy). Two cases are still under a close follow-up. One case of postpartum echocardiography result didn’t concord with the prenatal ultrasound diagnosis. Fourteen cases were lost from follow-up. Conclusion: Three-vessel-trachea view is a reliable view to diagnose fetal right aortic arch in prenatal ultrasonic examination, and simple fetal right aortic arch may not cause obvious clinical symptoms.
关键词
主动脉弓；胎儿疾病；超声检查 /
产前
Key words
Aorta, thoracic /
Fetal diseases /
Ultrasonography, prenatal
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