目的：探讨肝脏胆管错构瘤的MRI表现特点，提高对该病的认识及诊断。方法：选取两院确诊的13例成人肝脏胆管错构瘤作为研究对象，通过分析其MRI表现，对该病系统性分析。结果：3例行穿刺检查确诊。所有患者均呈弥漫多发病变，12例病灶弥漫分布肝脏左右两叶，1例弥漫分布于肝脏右叶；病变信号均匀，大小不等，多数病灶小于10 mm，呈长T1长T2囊性信号，DWI呈低信号，增强无强化。磁共振胰胆管造影（MRCP）显示病灶沿胆管树走行并与胆管树不相通。结论：肝脏胆管错构瘤在MRI扫描上有特异性表现，通过认识这些征象，提高对该病的诊断及鉴别诊断。
Abstract
Objective: To explore the MRI features of intrahepatic bile duct hamartoma in order to improve the understanding and diagnosis method of the disease. Methods: A total of 13 adult patients diagnosed by both hospital of intrahepatic bile duct hamartomas were enrolled and MRI features were analyzed systematically. Results: Three cases were confirmed by puncture. All patients were diffuse multiple lesions, 12 cases of diffuse lesions of liver two lobes, 1 case of diffuse distribution in the right lobe of liver; with uniform signal and unequal in size. The majority of lesions were less than 10 mm, showed as long T1 and long T2 cystic signal, DWI signal was low, no enhancement on contrast-enhanced imaging, MRCP showed lesions along the biliary tree and without connection between biliary tree. Conclusion: The liver bile duct hamartoma in MRI scans have specific performance, through the understanding of these signs to improve the diagnosis and different diagnosis of the disease.
关键词
肝肿瘤 /
错构瘤 /
磁共振成像 /
诊断 /
鉴别
Key words
Liver neoplasms /
Hamartoma /
Magnetic resonance imaging /
Diagnosis, differential
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