目的：探讨原发性椎管内恶性外周神经鞘膜瘤的MRI表现特点，提高该病的影像诊断水平。方法：回顾性分析经手术及病理证实的4例椎管内恶性外周神经鞘膜瘤的临床、MRI和病理表现，复习并总结相关文献。结果：4例椎管内恶性外周神经鞘膜瘤MRI表现均为混杂信号实性软组织肿块，其中瘤体较大者偏居椎管一侧，相邻椎间孔扩大，横跨椎管内外，形态似哑铃状，余呈类椭圆形；肿瘤边界尚清，增强扫描呈不均匀明显强化。结论：椎管内恶性外周神经鞘膜瘤是一种少见的恶性神经源性肿瘤，MRI对其诊断及鉴别诊断有一定价值。
Abstract
Objective: Imaging features of intraspinal malignant peripheral nerve sheath tumors(MPNST) was studied in order to increase diagnose level. Methods: We analyzed retrospectively the clinical manifestations, pathological and imaging features of four intraspinal MPNST patients who were proved pathologically, and reviewed related literatures at the same time. Results: The lesions of all four cases presented as heterogeneous solid mass. The bigger ones were partially in the vertebral canal side with adjacent intervertebral foramen, which were across the canal. The shape of tumors were dumbbell-like or oval with clearly boundary and obviously heterogeneous enhancement on MRI. Conclusion: MRI is of great value in the diagnosis and differential diagnosis of intraspinal MPNST.
关键词
脊椎肿瘤 /
神经鞘瘤 /
磁共振成像
Key words
Spinal neoplasms /
Neurilemmoma /
Magnetic resonance imaging
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